Pediatric and Young Adult GIST Data

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Reports - All under 30 | Carney's Triad | Pediatric GIST (under 18) | 18 to 24 years old | 25 to 30 years old

Life Raft Group Data

This table lists all of the Life Raft Group members under the age of 30. It is important to note that this group consists of several subgroups; under 18, Carney's Triad, 18 to 2 and 25 to 30. The natural course of the disease will vary between these subtypes and between individual patients.

All LRG patient members under age 30
Patient ID	Gender	Misdiagnosed Gist?	Original Cancer Diagnosis	Age at diagnosis	GIST Type	Mutation	Location of Primary Tumor at Diagnosis	Current age	Current Treatment
PG-131	F	FALSE	GIST	11.2	Carney's Triad	Wildtype	Stomach	14.1	None
PG-106	F	FALSE	GIST	12.6	Carney's Triad	Wildtype	Stomach	18.7	None
PG-115	F	FALSE	GIST	14.4	Carney's Triad	Wildtype	Stomach	17.1	None, Mets debulked
PG-125	F	TRUE	LMS	14.9	Carney's Triad	Wildtype	Stomach	30.0	Gleevec 800 mg (long-term)
PG-109	F	TRUE	GIST	15.9	Carney's Triad	Wildtype	Stomach	21.0	None
PG-133	F	FALSE	GIST	28.9	Carney's Triad	Wildtype	Stomach	30.2	Sutent 31.5 mg (Alternates 37.5 & 25)
PG-148	F	FALSE	GIST	30.4	Carney's Triad		Stomach	34.4	?
PG-136	F	FALSE	GIST	34.1	Carney's Triad	Wildtype	Stomach	34.5	None, has chondromas
PG-122	M	FALSE	GIST	17.9	Familial	Kit, exon 11	Small Bowel	19.3	None, NED
PG-120	F	TRUE	Other	7.7	GIST	Wildtype	Stomach	9.8	None, NED
PG-103	F	FALSE	GIST	8.2	GIST	Wildtype	Stomach	12.0	Sutent 25 mg 4/2 schedule
PG-124	F	FALSE	GIST	9.8	GIST		Stomach	11.4	None, NED
PG-137	M	FALSE	GIST	10.0	GIST		Unknown	10.5	None, NED
PG-110	F	FALSE	GIST	10.0	GIST	Wildtype	Stomach	15.4	Sutent 37.5 mg 4/2 schedule
PG-111	F	TRUE	LMS	10.4	GIST	Wildtype	Stomach	22.4	None NED
PG-127	F	FALSE	GIST	10.8	GIST		Stomach	15.7	None, 1 esophageal tumor remaining
PG-112	M	FALSE	GIST	12.3	GIST		Stomach	17.1	None, mets
PG-107	F	TRUE	LMS	12.4	GIST	Wildtype	Stomach	24.7	Gleevec
PG-121	F	TRUE	LMS	12.8	GIST		Stomach	31.6	None?
PG-104	F	FALSE	GIST	13.3	GIST		Stomach	17.7	None, NED
PG-114	M	FALSE	GIST	14.0	GIST		Stomach	16.5	Gleevec 600 mg, mets
PG-101	F	FALSE	GIST	15.3	GIST		Stomach	20.6	Sutent 12.5 mg
PG-132	M	FALSE	GIST	16.1	GIST	Wildtype	Stomach	16.5	Gleevec 500 mg
PG-135	M	FALSE	GIST	18.0	GIST	Wildtype	Stomach	19.6	None, NED
PG-117	F	TRUE	Other	19.2	GIST		Stomach	32.2	Gleevec 400 mg
PG-118	M	FALSE	GIST	19.3	GIST		Stomach	22.3	none, finished adjuvant Gleevec (1 yr)
PG-139	F	FALSE	GIST	19.5	GIST		Stomach	21.1	Neoadjuvant Gleevec 800 mg
PG-100	F	FALSE	GIST	19.6	GIST		Stomach	23.3	None
PG-138	F	TRUE	Other	19.9	GIST	Wildtype	Stomach	34.5	Sutent 31.5 mg (Alternates 37.5 & 25)
PG-108	F	TRUE	Other	20.3	GIST		Small Bowel	29.0	None, NED
PG-102	F	FALSE	GIST	20.6	GIST		Stomach	25.8	Deceased
PG-105	F	FALSE	GIST	21.0	GIST	Wildtype	Stomach	25.5	Sutent 50 mg 4/2 schedule
PG-130	F	FALSE	GIST	21.1	GIST		Stomach	21.8	Gleevec
PG-126	M	FALSE	GIST	21.8	GIST		Small Bowel	23.0	Gleevec 400 mg adjuvant
PG-149	F	FALSE	GIST	22.6	GIST		Stomach	31.5	Deceased
PG-116	M	FALSE	GIST	23.1	GIST		Liver	26.1	Deceased
PG-147	F	TRUE	LMS	23.7	GIST		Stomach	39.9	Deceased
PG-128	M	FALSE	GIST	23.9	GIST		Stomach	27.7	Gleevec + Rapamycin
PG-129	F	FALSE	GIST	24.6	GIST		Stomach	30.7	Gleevec + Rapamycin
PG-123	F	TRUE	Other	25.1	GIST	Wildtype	Stomach	42.3	None
PG-134	M	TRUE	Other	26.0	GIST		Small Bowel	35.2	Sutent 50 mg
PG-150	F	FALSE	GIST	26.3	GIST		Small Bowel	30.0	Gleevec 800 mg
PG-152	M	TRUE	Other	26.6	GIST		Large Bowel	28.4	Gleevec 800 mg (responding well)
PG-141	F	FALSE	GIST	26.7	GIST		Small Bowel	28.8	None, NED
PG-142	F	FALSE	GIST	27.1	GIST	Kit, exon 9	Small Bowel	28.3	Gleevec 600 mg adjuvant
PG-154	M	FALSE	GIST	27.6	GIST		Small Bowel	30.6	None, took adjuvant Gleevec for almost 3 years
PG-145	M	FALSE	GIST	27.7	GIST		Stomach	27.9	Sutent
PG-146	M	FALSE	GIST	28.2	GIST		Stomach	30.2	None
PG-155	M	FALSE	GIST	28.2	GIST			36.9	None
PG-143	F	FALSE	GIST	28.5	GIST		Abdomen	31.0	None, NED
PG-153	F	FALSE	GIST	28.8	GIST		Small Bowel	33.1	none, had mets, now NED
PG-144	F	FALSE	GIST	28.9	GIST		Stomach	28.9	None, NED
PG-140	M	FALSE	GIST	29.1	GIST	Kit	Small Bowel	31.7	Deceased
PG-156	F	FALSE	GIST	29.7	GIST		Stomach	35.4	Sutent 37.5 mg 4/2 schedule
PG-151	F		GIST		GIST		Stomach		Deceased
PG-157	M								Deceased

This pediatric portion of the website is dedicated to the memory of Jonathan Montague

1. Gastrointestinal Stromal Tumors in Children and Young Adults.
A Clinicopathologic, Molecular, and Genomic Study of 15 Cases and Review of the Literature. J Pediatr Hematol Oncol Volume 27, Number 4, April 2005. Sonam Prakash, MD, Lisa Sarran, MS, Nicholas Socci, PhD, Ronald P. DeMatteo, MD, Jonathan Eisenstat, MD, Alba M. Greco, MD,
Robert G. Maki, MD, PhD,{ Leonard H. Wexler, MD,k Michael P. LaQuaglia, MD, Peter Besmer, PhD, and Cristina R. Antonescu, MD